The aim of the study was to present and discuss the results of surgical treatment of congenital spherocytois in our department.Material and methods. Between 1994 and 2001 in the Department of General and Endocrinological Surgery at the Medical University in Białystok, 14 surgical excisions of enlarged spleens were performed because of congenital spherocytosis. The patients included five men and nine women aged between 17 and 61.Results. Diagnosis; non-surgical treatment and principles governing the decicion to use surgical intervention were evaluated by the Department of Hematology. Histopathological examinations for all cases confirmed the diagnosis of congenital spherocytosis.Conclusions. The undertaking of carefully considered procedures by the surgeons and hematologists in our departments resulted in propitious results in all the cases presented.