Full-text resources of PSJD and other databases are now available in the new Library of Science.
Visit https://bibliotekanauki.pl

PL EN


Preferences help
enabled [disable] Abstract
Number of results
2008 | 80 | 3 | 146-152

Article title

Surgeons' and Hematologists' Decisions on Splenectomy in the Treatment of Congenital Spherocytosis

Content

Title variants

Languages of publication

EN

Abstracts

EN
The aim of the study was to present and discuss the results of surgical treatment of congenital spherocytois in our department.Material and methods. Between 1994 and 2001 in the Department of General and Endocrinological Surgery at the Medical University in Białystok, 14 surgical excisions of enlarged spleens were performed because of congenital spherocytosis. The patients included five men and nine women aged between 17 and 61.Results. Diagnosis; non-surgical treatment and principles governing the decicion to use surgical intervention were evaluated by the Department of Hematology. Histopathological examinations for all cases confirmed the diagnosis of congenital spherocytosis.Conclusions. The undertaking of carefully considered procedures by the surgeons and hematologists in our departments resulted in propitious results in all the cases presented.

Year

Volume

80

Issue

3

Pages

146-152

Physical description

Dates

published
1 - 3 - 2008
online
7 - 4 - 2008

Contributors

author
  • 1st Department of General and Endocrinological Surgery, Medical University, Białystok
author
  • 1st Department of General and Endocrinological Surgery, Medical University, Białystok
  • 1st Department of General and Endocrinological Surgery, Medical University, Białystok
  • 1st Department of General and Endocrinological Surgery, Medical University, Białystok
  • 1st Department of General and Endocrinological Surgery, Medical University, Białystok
author
  • Department of Hematology, Medical University, Białystok
  • 1st Department of General and Endocrinological Surgery, Medical University, Białystok
  • 1st Department of General and Endocrinological Surgery, Medical University, Białystok

References

  • Bolton-Maggs PH: Hereditary spherocytosis; new guidelines. Arch Dis Child 2004; 89: 809-12.
  • Gallagher PG, Ferreira JD, Costa FF et al.: A reccurrent frameshift mutation of the ankyrin gene associated with severe hereditary spherocytosis. Br J Hematol 2000; 111(4): 1190-93.
  • Gallagher PG, Sabatino DE, Basseres DS et al.: Erythrocyte ankyrin promoter mutations associated with recessive hereditary spherocytosis cause significant abnormalities in ankyrin expression. J Biol Chem 2001; 9; 276(45): 41683-89.
  • Gnysta A, Agarwal S: Hereditary spherocytosis: diagnosis, prevention and treatment of spheres in genetic roll. Ind J Clin Pract 2002; 13(1): 17-24.
  • Rudowski W, Scharf R, Ziemski JR et al.: Splenectomy in the treatment of congenital spherocytosis. Indian J Surg 1981; 43: 393-97.
  • Nakamyshi H, Kauzaki A, Yawata A et al.: Ankyrin gen nutation in Japanese patients with hereditary spherocytosis. Int J Haematol 2001; 73(1): 54-63.
  • Valentine WN: Hereditary spherocytosis revisited. West J Med 1978; 128: 35-40.
  • Kwietniak JK: Splenektomia i jej wpływ na układ krwiotwórczy i zachowanie się odporności nieswoistej u ludzi zdrowych, z chorobami krwi oraz u zwierząt doświadczalnych (rozprawa). Sekcja Nauk Medycznych Polskiej Akademii Nauk 1965; Vol. 1.
  • Robak T (red.): Hematologia kliniczna w zarysie. Akademia Medyczna w Łodzi 1998: 64-65.
  • Scharf R. Chirurgia śledziony. W: Podstawy chirurgii. T. II. Szmidt J, Gruca Z, Krawczyk M i wsp. (red.). Medycyna Praktyczna, Kraków 2004; 1025-33.
  • Żukrowski P, Kielan W, Grzebieniak Z et al.: Splenectomy in Patients with Hematological Disorders - Our Experience. Pol J Surg 2007; 79: 426-35.
  • Puchalski Z, Róg M: Chirurgia pod red. W. Noszczyka, Wyd. 1. Wydawnictwo Lekarskie PZWL, Warszawa 2005; t. 2: 922-27.
  • Hughes-Jones NC, Wickramasinghe SN: W: Hematologia kliniczna w zarysie (pod red. K. Sułka. Wydawnictwo Medyczne Urban & Partner, Wrocław 2000: 50-52.
  • Singer DB: Postsplenectomy sepsis. W: Rosenberg HS, Bollande RP(eds.) Perspectives in pediatric pathology. Year Book Med. Publ. Chicago 1973.
  • Rosen M, Brody F, Walsh RM et al.: Outcome of laparoscopic splenectomy based on hematologic indication. Surg Endosc 2002; 16(2): 272-79.[Crossref]
  • Choi YS, Han HS, Yoon YS et al.: Laparoscopic splenectomy plus cholecystectomy for treating hereditary spherocytosis combined with cholelithiasis in siblings. Surg Endosc 2008; 22(1): 45-49.
  • Misiak A, Szczepaniak A, Huszcza S i wsp.: Splenektomia laparoskopowa a splenektomia klasyczna w małopłytkowości samoistnej - porównanie kosztów i ocena wczesnych wyników. Pol Przegl Chir 2004; 6: 607-17.
  • Bellows CF, Sweeney JF: Laparoscopic splenectomy: present status and future perspective. Expert Rev Med Devices 2006; 3: 95-104.[Crossref][PubMed]
  • Patel AG, Parker JE, Wallwork B et al.: Massive Splenomegaly Is Associated With Significant Morbidity After Laparoscopic Splenectomy. Ann Surg 2003; 238(2): 235-40.
  • Pawelski S, Rudowski W, Konopka L i wsp.: Hematologiczne i chirurgiczne problemy związane ze splenektomią u osób starszych. Acta Hematol Pol. 1976; 2: 129-33.
  • Dacie JV: The haemolytic anaemias. W: The congenital anaemias. Churchil (eds.) London 1970.
  • Krivit W, Giebink G, Leonard A: Overwhelming postsplenectomy infection. Surg Clin North Am 1979; 59: 223-28.
  • Constantinopoulus A: Defective phagocytosis due to tuftsin deficiency in splenectomized subject. Am J Dis Child 1973; 125: 663-70.
  • Najjar VA: The clinical and physiological aspects of tuftsin deficiency syndromes exhibiting defective phagocytosis. Klin Wochenschr 1979; 57: 751-56.
  • Schilling RF: Hereditary spherocytosis: a study of splenectomized persons. Semin Hematol 1976; 13: 169-73.[PubMed]
  • Fontan FJP, Soler R, Santos M et al.: Accessory spleen torsion: US, CT and MR findings, Eur Radiol 2001; 11: 509-12.
  • Cowles R, Lazar E. Symptomatic pelvic accessory spleen. Am J Surg 2007; 194: 225-26.[WoS]
  • Chapman RG: Red cell life span after splenectomy in hereditary spherocytosis. J Clin Invest 1968; 47: 2263-67.
  • MacKenzie FA, Eastocott HH, Eliot DH et al.: Relapse in hereditary spherocytosis with proven splenenculus. Lancet 1962; 1: 1102-03.
  • Gonzales G: Spherocytosis hereditary. Med J 2002; V. 3: N. 4.

Document Type

Publication order reference

Identifiers

YADDA identifier

bwmeta1.element.-psjd-doi-10_2478_v10035-008-0017-2
JavaScript is turned off in your web browser. Turn it on to take full advantage of this site, then refresh the page.