A rare cause of carpal tunnel syndrome in childhood: Benign recurrent intrahepatic cholestasis

• Authors: Necati Balamtekin , Nuray Uslu , Cagri Temucin , Hulya Demir , Inci Saltik Temizel
• Languages of publication: EN

Abstracts

EN

Carpal tunnel syndrome and benign recurrent intrahepatic cholestasis are rare conditions in childhood. Benign intrahepatic cholestasis is characterized by repeated self-limited attacks of cholestasis that can start at any age and last from weeks to months. The patients are asymptomatic between these attacks. We report a 16 year-old male patient with benign recurrent intrahepatic cholestasis who developed carpal tunnel syndrome during a cholestatic attack. He was admitted with complaints of jaundice, pruritus and pain, tingling and muscle weakness in both hands for 15 days. Nerve conduction studies revealed findings compatible with carpal tunnel syndrome. He was started on ursodeoxycholic acid, fat soluble vitamins and cholestyramine and cholestasis regressed after four weeks of therapy. With the improvement of cholestasis, the symptoms of carpal tunnel syndrome also disappeared. In conclusion, benign recurrent intrahepatic cholestasis can be a rare cause of carpal tunnel syndrome in childhood. We also advocate treating the underlying disease as an appropriate conservative treatment before surgery.

Keywords

EN

Child; Carpal tunnel syndrome; Benign recurrent intrahepatic cholestasis

• Publisher: De Gruyter Open
• Journal: Open Medicine
• Year: 2010
• Volume: 5
• Issue: 6
• Pages: 742-744

Dates

published

1 - 12 - 2010

online

7 - 10 - 2010

Contributors

author

Necati Balamtekin

• Faculty of Medicine, Department of Pediatrics, Section of Gastroenterology, Hepatology and Nutrition, Hacettepe University, 06100, Ankara, Turkey

author

Nuray Uslu

• Faculty of Medicine, Department of Pediatrics, Section of Gastroenterology, Hepatology and Nutrition, Hacettepe University, 06100, Ankara, Turkey

author

Cagri Temucin

• Faculty of Medicine, Department of Neurology, Hacettepe University, 06100, Ankara, Turkey

author

Hulya Demir

• Faculty of Medicine, Department of Pediatrics, Section of Gastroenterology, Hepatology and Nutrition, Hacettepe University, 06100, Ankara, Turkey

author

Inci Saltik Temizel

• Faculty of Medicine, Department of Pediatrics, Section of Gastroenterology, Hepatology and Nutrition, Hacettepe University, 06100, Ankara, Turkey

References

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Identifiers

DOI

10.2478/s11536-009-0142-2