Henoch-Schönlein purpura presenting with multiplex gastrointestinal manifestations and massive nephrotic syndrome in adulthood - a case report

• Authors: Farkas Klaudia , Molnár Tamás , Nagy Ferenc , Tiszlavicz László , Németh István , Kemény Éva , Varga Erika , Wittmann Tibor
• Languages of publication: EN

Abstracts

EN

Henoch-Schönlein purpura (HSP) is a systemic small vessel vasculitis mainly affecting children. We report a case of a 49-year-old woman with severe gastrointestinal and renal involvement of HSP. Endoscopy revealed more characteristic findings in the terminal ileum than in the gastric antrum. Histological examinations of the biopsy samples from the ileum, antrum, skin and kidney confirmed the diagnosis of HSP. Parenteral corticosteroid therapy led to a rapid improvement of the gastrointestinal symptoms, but because of the excessive proteinuria intravenous cyclophosphamide therapy had to be introduced.

Keywords

EN

Henoch-Schönlein purpura; Nephrotic syndrome; Adulthood

• Publisher: De Gruyter Open
• Journal: Open Medicine
• Year: 2008
• Volume: 3
• Issue: 4
• Pages: 521-524

Dates

published

1 - 12 - 2008

online

22 - 10 - 2008

Contributors

author

Farkas Klaudia

• First Department of Internal Medicine, University of Szeged, H6720, Szeged, Hungary

author

Molnár Tamás

• First Department of Internal Medicine, University of Szeged, H6720, Szeged, Hungary

author

Nagy Ferenc

• First Department of Internal Medicine, University of Szeged, H6720, Szeged, Hungary

author

Tiszlavicz László

• Department of Pathology, University of Szeged, H6720, Szeged, Hungary

author

Németh István

• Department of Pathology, University of Szeged, H6720, Szeged, Hungary

author

Kemény Éva

• Department of Pathology, University of Szeged, H6720, Szeged, Hungary

author

Varga Erika

• Department of Dermatology and Allergology, University of Szeged, H6720, Szeged, Hungary

author

Wittmann Tibor

• First Department of Internal Medicine, University of Szeged, H6720, Szeged, Hungary

References

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Identifiers

DOI

10.2478/s11536-008-0060-8