A case of Multiple Unilateral Pulmonary arteriovenous Malformation Relapse: Efficacy of embolization treatment

• Authors: Rossella Masiello , Carlo Iadevaia , Edoardo Grella , Carmelindo Tranfa , Francesco Cerqua , Giovanni Rossi , Giuseppe Santoro , Bruno Amato , Aldo Rocca , Roberta De Dona , Sabrina Lavoretano , Fabio Perrotta
• Languages of publication: EN

Abstracts

EN

Pulmonary arteriovenous Malformations (PAVMs) are a rare vascular alteration characterized by abnormal communications between the pulmonary arteries and veins resulting in an extracardiac right-to-left (R-L) shunt. The majority of PAVMs are associated with an autosomal dominant vascular disorder also known as Osler-Weber- Rendu Syndrome. PAVMs appearance can be both single and multiple. Clinical manifestations include hypoxemia, dyspnea cyanosis, hemoptysis and cerebrovascular ischemic events or abscesses. We report a case of an 18 year old female with severe respiratory failure caused by a relapse of multiple unilateral pulmonary arterovenous fistula. Symptoms at admission include dyspnea, cyanosis and clubbing. The patient underwent pulmonary angio-TC scan, brain CT and echocardiography. The thoracic angio-CT scan showed the presence of PAVMs of RUL and RLL; a marked increase of right bronchial artery caliber and its branches with an aneurismatic dilatation was also observed. The patient underwent percutaneous transcatheter embolization using Amplatzer Vascular Plug IV; a relevant clinical and functional improvement was subsequently recorded. Embolization is effective in the treatment of relapsing PAVMS.

Keywords

EN

Pulmonary arteriovenous Malformations (PAVMs); Embolization; Unilateral fistula; Angio-CT Scan

• Publisher: De Gruyter Open
• Journal: Open Medicine
• Year: 2014
• Volume: 10
• Issue: 1

Dates

published

1 - 1 - 2015

online

17 - 12 - 2015

received

26 - 10 - 2015

accepted

4 - 11 - 2015

Contributors

author

Rossella Masiello

• Department of Cardio- Thoracic and Respiratory Sciences – Second University of Naples - Monaldi Hospital, Naples, Italy Giovanni Rossi: U.O.C. Radiology A.O.R.N dei Colli – Monaldi Hospital, Naples, Italy

author

Carlo Iadevaia

• Department of Cardio- Thoracic and Respiratory Sciences – Second University of Naples - Monaldi Hospital, Naples, Italy

author

Edoardo Grella

• Department of Cardio- Thoracic and Respiratory Sciences – Second University of Naples - Monaldi Hospital, Naples, Italy

author

Carmelindo Tranfa

• Department of Cardio- Thoracic and Respiratory Sciences – Second University of Naples - Monaldi Hospital, Naples, Italy

author

Francesco Cerqua

• Department of Cardio- Thoracic and Respiratory Sciences – Second University of Naples - Monaldi Hospital, Naples, Italy

author

Giovanni Rossi

• U.O.C. Radiology A.O.R.N dei Colli – Monaldi Hospital, Naples, Italy

author

Giuseppe Santoro

• Department of Cardio- Thoracic and Respiratory Sciences – Second University of Naples - Monaldi Hospital, Naples, Italy

author

Bruno Amato

• Department of Clinical Medicine and Surgery, University of Naples Federico II, Italy

author

Aldo Rocca

• Department of Clinical Medicine and Surgery, University of Naples Federico II, Italy

author

Roberta De Dona

• Department of Medicine and Health Sciences “V. Tiberio”, University of Molise, Campobasso, Italy

author

Sabrina Lavoretano

• Department of Medicine and Health Sciences “V. Tiberio”, University of Molise, Campobasso, Italy

author

Fabio Perrotta

• Department of Cardio- Thoracic and Respiratory Sciences – Second University of Naples - Monaldi Hospital, Naples, Italy

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Identifiers

DOI

10.1515/med-2015-0087