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2018 | 23 | 4 | 199-204
Article title

Podsumowanie zaleceń postępowania we wrodzonym obrzęku naczynioruchowym z niedoboru C1 inhibitora

Content
Title variants
EN
Summary of recommendations for the management of hereditary angioedema due to C1 inhibitor deficiency
Languages of publication
PL EN
Abstracts
EN
The paper summarizes the recommendations of the Hereditary Angioedema Section of the Polish Society of Allergology regarding the management of this disease in a view on up-to-date data. Its classification, pathomechanism, clinical picture and diagnosis were discussed. The principles of treatment and prevention of edema attacks and disease monitoring were presented. Characteristic features related to the course and management during pregnancy and in the pediatric group of patients were mentioned.
PL
W pracy podsumowano, w świetle zaktualizowanych danych, zalecenia Sekcji Wrodzonego Obrzęku Naczynioruchowego Polskiego Towarzystwa Alergologicznego dotyczące postępowania w tym schorzeniu. Omówiono jego klasyfikację, patomechanizm, obraz kliniczny i rozpoznawanie. Przedstawiono zasady leczenia i zapobiegania napadom obrzęku oraz monitorowania choroby. Wymieniono cechy charakterystyczne odnoszące się do przebiegu i postępowania w okresie ciąży i w pediatrycznej grupie chorych.
Discipline
Publisher

Year
Volume
23
Issue
4
Pages
199-204
Physical description
Contributors
  • Zakład Alergologii Klinicznej i Środowiskowej, Uniwersytet Jagielloński Collegium Medicum w Krakowie
  • Zakład Alergologii Klinicznej i Środowiskowej, Uniwersytet Jagielloński Collegium Medicum w Krakowie
  • Zakład Alergologii Klinicznej i Środowiskowej, Uniwersytet Jagielloński Collegium Medicum w Krakowie
  • Zakład Alergologii Klinicznej i Środowiskowej, Uniwersytet Jagielloński Collegium Medicum w Krakowie
References
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Document Type
article
Publication order reference
Identifiers
YADDA identifier
bwmeta1.element.psjd-f8184f63-e633-4952-b400-1a75eb441ed2
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