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2019 | 1 | 2 | 4-10
Article title

Pediatric cardiology emergencies – the role of Long QT Syndrome among arrhythmias

Content
Title variants
Languages of publication
EN
Abstracts
EN
Long QT syndrome (LQTS) is a hereditary disease with significant mortality, which might be reduced with appropriate management. This cardiac disorder is regarded as rare, but its prevalence remains unknown. The clinical course of LQTS is variable and syncope is a common first manifestation of LQTS. Therefore in each patient after syncope an ECG should be carried out. However, there is no universal QT value applying to all patients (especially infants and children), because it varies depending on age and sex. Genetic testing can be of great importance for the management of families with LQTS and early identification of patient relatives at risk of developing disease. We aimed to show that a very important part of treatment is not only pharmacotherapy, especially beta-blockers, but change of lifestyle plays a significant role.
Year
Volume
1
Issue
2
Pages
4-10
Physical description
Dates
published
2019-02-05
received
2019-01-15
accepted
2019-01-29
References
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Document Type
Publication order reference
Identifiers
YADDA identifier
bwmeta1.element.doi-10_31373_ejtcm_103441
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