In August 2003, a 15 year old male, with a giant tumor located on the whole left side of his face, was admitted for treatment. The changes in appearance first began to show in the 2nd month after birth and systematic enlargement lead to an overgrowth of the soft tissues and bones of the face. As a result of the pressure excerted by the tumor, the frontal bone and the surrounding protective structures became thickened and displaced posterio-inferiorly, causing a shrinking of the anterio-inferior part of the skull. Histological analysis indicated that the tumor was of neurological origin. The patient was operated on a year later because of the continued growth of the tumor. Another year later, the enlarged and protruding maxillar bone was filed down.A radical approach is important in such cases, not only from an aesthetic point of view, but most of all because it is the best way of counteracting any regrowth of the tumour and is the most effective means of oncological prophylaxis.