Solid pseudopapillary tumor (SPT) is a rare pancreatic neoplasm of unspecified origin that occurs most frequently in young women. In most patients, it has a benign character.In study presented a description of the case of a 36-year-old patient operated due to SPT in 2004. The patient had an atypical clinical course of the disease with a double relapse of the neoplastic process, which was operated on in 2006 and 2007.The symptoms and clinical course of SPT are characterized by very high interpersonal variation. Therefore, it is necessary to deepen the knowledge of the histogenesis and biology of the tumor. Additionally, the patients who receive surgery due to the tumor must be observed for many years.