Mediastinal lymphangioma and generalized lymphangiomatosis a case report

• Authors: Edin Jusufovic , Dragan Keser , Edin Zukic
• Languages of publication: EN

Abstracts

EN

Lymphangioma is a malformation composed of a mass of dilated lymph vessels typically found in the cervical region in children. Mediastinal lymphangioma is a rare condition and accounts for 0.01% to 4.5% of all mediastinal tumors. Only 4 cases of mediastinal lymphangioma involving the heart and great vessels in adults have been described in the available literature. Extremely rarely, lymphangiomas occur as a generalized lymphangiomatosis. We present a case of a woman who coughed up small amounts of fresh blood during 6 months and showed signs of cardiac failure. Several years previously, the patient underwent surgical removal of cystic lymphangiomas from the left ovary, both fallopian tubes and small intestine. A chest radiograph showed an 8-cm round shadow located in the middle lobe. A computerized tomography (CT) scan of the chest with contrast verified the existence of a cyst in the anterior mediastinum. The radiologist suggested that the cyst could have originated in the pericardium. One small cyst also appeared in the projection of the left cardiophrenic sinus. A CT scan with contrast of the patient’s abdomen showed multiple cystic formations in the liver, spleen, kidneys, and left parapelvic region. A fine-needle biopsy of the mediastinal tumor verified the cystic lymphangioma, which was then completely removed surgically. A pathohistological examination confirmed the existence of cystic lymphangioma. The patient was discharged after a period of recovery.

Keywords

EN

Lymphangioma; Mediastinum; Generalized lymphangiomatosis

• Publisher: De Gruyter Open
• Journal: Open Medicine
• Year: 2011
• Volume: 6
• Issue: 3
• Pages: 289-293

Dates

published

1 - 6 - 2011

online

8 - 4 - 2011

Contributors

author

Edin Jusufovic

author

Dragan Keser

author

Edin Zukic

• Polyclinic for lung disease, The Health Centre Tuzla, Albina Herljevica 1, 75000, Tuzla, Bosnia and Herzegovina

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Identifiers

DOI

10.2478/s11536-011-0009-1